DISCUSSION
Scimitar syndrome, a rare congenital defect, is characterised by partial or complete anomalous pulmonary venous return from the right lung into the systemic venous system. Its presentation varies from asymptomatic state, dyspnoea and recurrent pulmonary infections in adults to severe pulmonary hypertension and heart failure with associated congenital heart defects in infants.1 The ‘scimitar’ sign, a term meaning curved eastern sword, is a characteristic radiographic finding of a crescent-like shadow in the right lower lung field, due to the anomalous vein.2 The diagnostic modalities include chest X-ray, cardiac echocardiography, CT, MRI and angiography. Presence of congestive heart failure, recurrent pneumonias, pulmonary/systemic blood flow ratio > 1.5 and pulmonary hypertension warrants surgical correction.1
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