Issue: 2017 > January > case report

IgG4-related disease: a disease we probably often overlook

I.M. Celis, R.L. Kriekaart, R.P. Aliredjo, E.G. van Lochem, M.J.D.L. van der Vorst, R. Hassing
AbstractFull textPDF


IgG4-related disease (IgG4-RD) is an increasingly recognised entity characterised by tumefied lesions that can affect multiple organs. Awareness of IgG4-RD is important, as it has been shown to mimic other diseases and may result in irreversible organ damage if not treated. If suspected, immunostaining for IgG4-positive plasma cells is essential for diagnosis and revision of old biopsies may be necessary.