Issue: 2020 > April > case report

Case series of three adult patients with exceptional clinical presentations of haemophagocytic lymphohistiocytosis

M. Khairoun, F. Meynen, W. Vercoutere, H.L. Leavis
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Macrophage activation syndrome (MAS) is a secondary form of haemophagocytic lymphohistiocytosis (HLH). MAS-HLH is an underrecognised and life-threatening condition associated with a heterogeneous group of diseases including connective tissue disease and inflammatory disorders. Here, we report three cases of adult patients with MAS-HLH triggered by different entities, including systemic lupus erythematosus, Griscelli syndrome type 2, and Adult onset Still’s disease.